Gastrointestinal stromal tumor

ICD-10: 2B12.0MeSH: D046128ORPHA: 44890

Overview

Gastrointestinal stromal tumor is a rare mesenchymal neoplasm of the gastrointestinal tract driven most often by activating mutations in KIT or PDGFRA, with a minority associated with SDH deficiency or other drivers. Symptoms depend on tumor site and size and may include abdominal pain, bleeding, early satiety, or incidental discovery on imaging. It is uncommon overall, and targeted tyrosine kinase inhibitors are documented treatment options in mutation-specific settings.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Gastrointestinal stromal tumor, sourced from HPO and Orphanet clinical annotations.

Skin rashAbnormality of the liverAnemiaDysphagiaNausea and vomitingConstipationGastrointestinal hemorrhageIntestinal obstructionNeoplasm of the stomachNeoplasm of the gastrointestinal tractIrregular hyperpigmentationFatigueSarcomaNeoplasm of the colonGastrointestinal stroma tumorNeoplasm of the rectumEsophageal neoplasmNeoplasm of the small intestine

Classification & Codes

ICD-10 Code

2B12.0

MeSH Code

D046128

Orphanet Code

ORPHA:44890
Gastrointestinal stromal tumor
ICD-102B12.0
MeSHD046128
OrphanetORPHA:44890
Treatments0 drug(s)
Symptoms on record18 signs
Statuspublished
Factual Authority
Last Updated7/24/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO