Hereditary Angioedema

ICD-10: D84.1MeSH: D054179ORPHA: 913851 Treatment Available

Overview

Hereditary angioedema is an autosomal dominant disorder caused by deficiency or dysfunction of C1 esterase inhibitor, leading to recurrent episodes of severe swelling affecting the skin, gastrointestinal tract, and upper airways. Three types are recognized: Type I (85% of cases) with low C1-INH levels, Type II with dysfunctional C1-INH, and Type III with normal C1-INH. The estimated prevalence is 1 in 50,000 individuals worldwide.

Available Treatments (1)

DrugFormStatusCountriesLead Time
garadacimab
Orphan Cold Chain
FDA Approved (2025)1

Classification & Codes

ICD-10 Code

D84.1

MeSH Code

D054179

Orphanet Code

ORPHA:91385
Hereditary Angioedema
ICD-10D84.1
MeSHD054179
OrphanetORPHA:91385
Treatments1 drug(s)
Statuspublished

Treatment Summary

Factual Authority
Last Updated3/21/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO