Tenosynovial Giant Cell Tumor
ICD-10: 2E80.YORPHA: ORPHA:1000751 Treatment Available
Overview
A rare, locally aggressive neoplasm of the synovium of joints, bursae, and tendon sheaths driven by CSF1 overexpression. Presents as localized or diffuse (pigmented villonodular synovitis) forms.
Available Treatments (1)
| Drug | Form | Status | Countries | Lead Time |
|---|---|---|---|---|
| vimseltinib Orphan | — | FDA Approved (2025) | 1 | — |
Classification & Codes
ICD-10 Code
2E80.YOrphanet Code
ORPHA:ORPHA:100075Tenosynovial Giant Cell Tumor
| ICD-10 | 2E80.Y |
| Orphanet | ORPHA:ORPHA:100075 |
| Treatments | 1 drug(s) |
| Status | published |
Treatment Summary
Factual Authority
Last Updated7/24/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO